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產(chǎn)品名稱：結(jié)蛋白（Anti-Desmin/DES）抗體【*】
中文名稱：結(jié)蛋白抗體
英文名稱：Anti-Desmin/DES
產(chǎn)品編號(hào)：BYK-1026R
產(chǎn)品別名：CMD1I; CSM1; CSM2; DES; FLJ12025; FLJ39719; FLJ41013; FLJ41793; Intermediate filament protein; OTTHUMP00000064865; DESM_HUMAN; Desmin; FLJ12025; FLJ39719; FLJ41013; FLJ41793.

本公司另供應(yīng)“結(jié)蛋白抗體”的標(biāo)記有：Alexa Fluor 350 Alexa Fluor 488 Alexa Fluor 555 Alexa Fluor 647 AP APC Biotin Cy3 Cy5 Cy5.5 Cy7 FITC Gold HRP PE PE-Cy3 PE-CY5 PE-CY5.5 PE-CY7 RBITC.
產(chǎn)品規(guī)格：100ug/200ug
產(chǎn)品濃度： 1mg/1ml
抗體來(lái)源：兔源、鼠源、其他
克 隆：?jiǎn)慰寺】贵w、多克隆抗體
抗體類型：一抗
性 狀： 凍干粉或液體
保存條件：Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.

結(jié)蛋白（Anti-Desmin/DES）抗體【*】技術(shù)說(shuō)明，產(chǎn)品*，由于篇幅原因，更多信息請(qǐng)：

Anti-CD13/FITC抗體，熒光素標(biāo)記氨肽酶N抗體IgG
Anti-CD14/FITC抗體，熒光素標(biāo)記CD14蛋白抗體IgG
Anti-CD17/FITC  熒光素標(biāo)記CD17抗體IgG
Anti-CD18/LFA-1/FITC  熒光素標(biāo)記白細(xì)胞粘附蛋白抗體IgG
Anti-CD19/FITC  熒光素標(biāo)記CD19抗體IgG
Anti-CD20/FITC  熒光素標(biāo)記CD20抗體IgG
Anti-CD20/Biotin  *化CD20抗體IgG
Anti-SLAMF9/CD2F-10/FITC抗體，熒光素標(biāo)記CD2F-10抗體IgG
Anti-CD3/FITC抗體，熒光素標(biāo)記CD3蛋白抗體IgG
Anti-CD3/RBITC抗體，紅色熒光素羅丹明標(biāo)記CD3抗體IgG
Anti-CD4/FITC抗體，熒光素標(biāo)記CD4蛋白抗體IgG
Anti-CD4/RBITC抗體，紅色熒光素羅丹明（RBITC）標(biāo)記CD4抗體IgG

Anti-CD22/FITC  熒光素標(biāo)記抗白細(xì)胞分化抗原CD22抗體IgG
Anti-CD23/FcεRⅡ/FITC  熒光素標(biāo)記CD23抗體IgG
Anti-CD24/FITC  熒光素標(biāo)記CD24蛋白抗體IgG
Anti-CD25/IL-2RA/FITC  熒光素標(biāo)記CD25/白介素2-受體抗體IgG
Anti-CD26/ADCP2/DPPⅣ/FITC  熒光素標(biāo)記CD26抗體IgG
Anti-CD27/TNFRSF7/FITC  熒光素標(biāo)記CD27抗體IgG
Anti-CD28/FITC  熒光素標(biāo)記CD28蛋白抗體IgG
Anti-CD6/TP120/FITC抗體，熒光素標(biāo)記CD6抗體IgG
Anti-CD7/FITC抗體，熒光素標(biāo)記抗CD7抗體IgG
Anti-CD8/FITC抗體，熒光素標(biāo)記CD8蛋白抗體IgG
Anti-CD9/MRP-1/FITC抗體，熒光素標(biāo)記CD9抗體IgG
Anti-CD10/CALLA/FITC抗體，熒光素標(biāo)記CD10抗體IgG

產(chǎn)品介紹：

filaments found in muscle cells. In adult striated muscle they form a fibrous network connecting myofibrils to each other and to the plasma membrane from the periphery of the Z line structures. Defects in Desmin are the cause of desmin related cardio skeletal myopathy （CSM） also known as desmin related myopathy （DRM）. CSM is characterized by skeletal muscle weakness associated with cardiac conduction blocks, arrhythmias, restrictive heart failure, and by intracytoplasmic accumulation of desmin reactive deposits in cardiac and skeletal muscle cells. A desmin related myopathy can have a distal onset, it is then known as hereditary distal myopathy （HDM）. Defects in Desmin are also the cause of dilated cardiomyopathy type 1I （CMD1I）. CMD1I is an autosomal form of dilated cardiomyopathy characterized by ventricular dilatation and impaired systolic function. Antidesmin antibodies are useful in identification of tumours of myogenic origin.