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產(chǎn)品名稱：Anti-SGSH/Sulphamidase巨額讓利,磺氨基葡糖硫酸胺酶抗體 
中文名稱：磺氨基葡糖硫酸胺酶抗體
英文名稱：Anti-SGSH/Sulphamidase
產(chǎn)品編號：BYK-11756R
產(chǎn)品別名：Heparan sulfate sulfatase; Heparan sulphate sulphatase; HSS; MPS 3A; MPS3 A; MPS3A; N sulfoglucosamine sulfohydrolase （sulfamidase）; N-sulphoglucosamine sulphohydrolase; SFMD; SGSH; SPHM_HUMAN; Sulfoglucosamine sulfamidase; Sulphamidase; Sulphoglucosamine sulphamidase.

本公司另供應(yīng)“磺氨基葡糖硫酸胺酶抗體”的標記有：Alexa Fluor 350 Alexa Fluor 488 Alexa Fluor 555 Alexa Fluor 647 AP APC Biotin Cy3 Cy5 Cy5.5 Cy7 FITC Gold HRP PE PE-Cy3 PE-CY5 PE-CY5.5 PE-CY7 RBITC.
產(chǎn)品規(guī)格：100ug/200ug
產(chǎn)品濃度： 1mg/1ml
抗體來源：兔源、鼠源、其他
克        隆：單克隆抗體、多克隆抗體
抗體類型：一抗
性        狀： 凍干粉或液體
保存條件：Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.

Anti-SGSH/Sulphamidase巨額讓利,磺氨基葡糖硫酸胺酶抗體技術(shù)說明，產(chǎn)品*，由于篇幅原因，更多信息請：

Anti-PS-1（CT）/FITC  熒光素標記早老素蛋白-1抗體IgG
Anti-PSAP/PAP/FITC  熒光素標記前列腺酸性磷酸酶抗體IgG
Anti-PSCA /FITC  熒光素標記抗前列腺干細胞抗原抗體IgG
Anti-PSD-95/FITC  熒光素標記突觸后密度蛋白95抗體IgG
Anti-P-selectin/CD62p /FITC  熒光素標記P選擇素抗體IgG
Anti-PSGL-1/CD162/FITC  熒光素標記P選擇素糖蛋白配體1抗體IgG
Anti-PSMD9/Bridge-1 /FITC  熒光素標記蛋白酶調(diào)解因子9抗體IgG
Anti-pre-X protein（NT）/FITC  熒光素標記抗乙肝病毒pre-X蛋白抗體（N端）IgG
Anti-pre-X protein（CT）/FITC  熒光素標記抗乙肝病毒pre-X蛋白抗體（C端）IgG

Anti-PSP/FITC  熒光素標記抗PSP抗體IgG
Anti-Ptch/FITC  熒光素標記Hh信號轉(zhuǎn)導(dǎo)途徑膜蛋白受體抗體IgG
Anti-PTEN/MMAC1（NT）/FITC  熒光素標記一種腫瘤抑制基因（N端）IgG
Anti-PTEN/MMAC1 /FITC  熒光素標記一種腫瘤抑制基因抗體（C端）IgG
Anti-PTGEs/FITC  熒光素標記前列腺素E合成酶抗體IgG
Anti-PTHrP/FITC  熒光素標記甲狀旁腺激素相關(guān)蛋白抗體IgG
Anti-Survivin/RBITC  紅色熒光素羅丹明標記 Survivin 蛋白抗體
Anti-pro-caspase3/FITC  熒光素標記半胱天冬酶-3酶原抗體IgG
Anti-Profilin 1/FITC  熒光素標記前纖維蛋白1抗體IgG
Anti-Profilin 2/FITC  熒光素標記前纖維蛋白2抗體IgG
Anti-PROK1/EG-VEGF/FITC  熒光素標記內(nèi)分泌腺衍生血管內(nèi)皮生長因子抗體IgG
Anti-Melamine/HRP  辣根過氧化物酶標記抗三聚氰胺抗體IgG
Anti-PS-1/FITC  熒光素標記早老素蛋白-1抗體IgG
Anti-PS-1/FITC  熒光素標記早老素蛋白-1抗體IgG

產(chǎn)品介紹：
Sulfatases are enzymes that hydrolyse a diverse range of sulfate esters. Deficiency of lysosomal sulfatases leads to human diseases characterized by the accumulation of either GAGs （glycosaminoglycans） or sulfolipids. Sulfamidase, also known as HSS, SFMD, MPS3A or SGSH, is a 502 amino acid lysosome that belongs to the sulfatase family. It has been suggested that sulfamidase may be involved in the lysosomal degradation of heparan sulfate. Defects in the gene encoding sulfamidase are the cause of Sanfilippo syndrome A, an autosomal recessive lysosomal storage disease caused by impaired degradation of heparan sulfate. Sanfilippo syndrome A is characterized by severe central nervous system degeneration but relatively mild somatic manifestations.