上海博研生物工程研究中心為您現(xiàn)貨提供*的產(chǎn)品與服務(wù)，本中心產(chǎn)品齊全，保證實驗的有效性，提供，是您科研實驗產(chǎn)品的一站式平臺，咨詢。！

產(chǎn)品名稱：Anti-TIMM8A抗體優(yōu)貨，線粒體內(nèi)膜轉(zhuǎn)位酶8A/肌張力障礙肽抗體

中文名稱：線粒體內(nèi)膜轉(zhuǎn)位酶8A/肌張力障礙肽抗體

英文名稱：Anti-TIMM8A

產(chǎn)品編號：BYK-11769R

產(chǎn)品別名：DDP 1; DDP; DDP1; Deafness dystonia protein 1; Deafness/dystonia peptide; DFN 1; DFN1; MGC12262; Mitochondrial import inner membrane translocase subunit Tim8 A; MTS; TIM 8A; TIM8A; TIMM 8A; Translocase of inner mitochondrial membrane 8 homolog A; X linked deafness dystonia protein; TIM8A_HUMAN.

本公司另供應(yīng)"Anti-TIMM8A抗體優(yōu)貨，線粒體內(nèi)膜轉(zhuǎn)位酶8A/肌張力障礙肽抗體”的標(biāo)記有：Alexa Fluor 350 Alexa Fluor 488 Alexa Fluor 555 Alexa Fluor 647 AP APC Biotin Cy3 Cy5 Cy5.5 Cy7 FITC Gold HRP PE PE-Cy3 PE-CY5 PE-CY5.5 PE-CY7 RBITC.
產(chǎn)品規(guī)格：100ug/200ug
產(chǎn)品濃度： 1mg/1ml
抗體來源：兔源、鼠源、山羊
克 ?。簡慰寺】贵w、多克隆抗體
抗體類型：一抗
性 狀： 凍干粉或液體
保存條件：Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.

技術(shù)說明，產(chǎn)品*，由于篇幅原因，更多信息請：
Anti-STAT6 /FITC  熒光素標(biāo)記信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子6抗體IgG
Anti-STEAP1/FITC  熒光素標(biāo)記前列腺跨膜上皮抗原1抗體IgG
Anti-Synaptophysin（SAP-1）/FITC  熒光素標(biāo)記抗突觸素抗體IgG
Anti-alpha-Synuclein/FITC  熒光素標(biāo)記核突觸蛋白-α抗體（C端）IgG
Anti-α-Synuclein/FITC  熒光素標(biāo)記核突觸蛋白-α抗體IgG
Anti-γ-Synuclein/SNCG /FITC  熒光素標(biāo)記核突觸蛋白-γ抗體IgG
Anti-Syntaxin 1/Syn1A /FITC  熒光素標(biāo)記突觸融合蛋白1抗體IgG
Anti-α-Synuclein/FITC  熒光素標(biāo)記核突觸蛋白/突觸素-1抗體IgG
Anti-SYPH1/FITC  熒光素標(biāo)記synphilin-1抗體IgG
Anti-SYVN1/FITC  熒光素標(biāo)記滑膜細(xì)胞凋亡抑制物1抗體IgG
Anti-TNF-α /Biotin  *標(biāo)記 腫瘤壞死因子抗體
Anti-T3/FITC  熒光素標(biāo)記三碘甲狀腺素T3抗體IgG
Anti-TACR3/NK-3 receptor /FITC  熒光素標(biāo)記速激肽受體3抗體IgG
Anti-Socs 3/FITC 熒光素標(biāo)記細(xì)胞因子信號傳導(dǎo)抑制蛋白3抗體IgG
Anti-SOD1/FITC 熒光素標(biāo)記超氧化物歧化酶1抗體IgG

產(chǎn)品介紹：

The majority of mitochondrial-directed proteins are encoded by the nuclear genome and are transported to the mitochondria via regulated processes involving the mitochondrial Tom and Tim proteins （1）. The mitochondrial Tim protein family is comprised of a large group of evolutionarily conserved proteins that are found in most eukaryotes （1,2）. Import of nuclear-encoded precursor proteins into and across the mitochondrial inner membrane is mediated by two distinct complexes, the Tim23 complex and the Tim22 complex, which differ in their substrate specificity （1）. Defects in Tim proteins are implicated in several neuro-degenerative diseases, suggesting important roles for Tim proteins in development and health （3,4）. Tim8A and Tim8B, which map to human chromosomes Xq22.1 and 11q23.1-q23.2, respectively, are conserved proteins of the mitochondrial intermembrane space, which are organized in hetero-oligomeric complex with Tim13 （5,6,7）. Tim8A is highly expressed in fetal and adult brain （5）. Tim8A is mutated in deafness dystonia syndrome, a novel type of disease that causes severe neurological defects, thought to be caused by a defective mitochondrial protein transport system （5,8）.